Aim: Here we present a rare case of Glomangiopericytoma of the nasal cavity and review the recent literature. This case is presented because of its rarity. Case report: A 36-year-old woman presented to the Outpatient Department of ENT and Head and Neck Surgery in a tertiary care centre with complaints of progressive unilateral nasal obstruction and anosmia over a 6 month period. Anterior rhinoscopicex amination revealed a pinkish globular mass occupying the left nasal cavity. Computed tomography (CT) scan revealed an ill defined homogenous soft tissue density lesion involving the left nasal cavity, infiltrating the nasal septum posteriorly and extending upto the choana with a deviated nasal septum to the right side. The tumor was resected completely by endoscopic approach. Histopathologic examination with immunohistochemistry of the resected mass confirmed the diagnosis of glomangiopericytoma. Discussion: Glomangiopericytoma is a rare sinonasal neoplasm characterized by a perivascular myoid phenotype and is considered as distinct from conventional soft tissue hemangiopericytoma. It accounts for less than 0.5% of all sinonasal tumors. It is classified as a borderline low malignancy tumor.Conclusion: This tumour is associated with a very good prognosis following surgery and complete surgical resection with negative margins preferably via a transnasal endoscopic approach is the treatment of choice.