Introduction: Arnold Chiari malformations are composite brain irregularities within the posterior cranial fossa where Cerebellum and Spinal cord associate. So herniation of the Cerebellum, Spinal cord and Cerebellar tonsils downwards through the foramen magnum will prevent the continuous flow of cerebrospinal fluid from the brain to the spinal canal which produces a collection of cerebrospinal fluid in subarachnoid space resulting in asymptomatic or fatal signs. Aim: To find out the associated findings in the detected case of Arnold-Chiari malformation. Case Report / Result: Out of Fifty specimens, one case of Arnold-Chiari malformation was reported having some features of Chiari Malformation Type 2. Discussion: Chiari malformation Type 2 is severe than Type 1. Symptoms appear only in childhood. Cerebellar herniation protrudes into the spinal canal producing Hydrocephalus. Chiari malformation type 2 is connected with a form of split spine and Myelomeningocele. Conclusion: One female child was reported with features of Type 2 Arnold Chiari malformation. Congenital anomalies are more observed in mothers of low socioeconomic groups, increasing maternal age and a history of consanguineous marriage.