Background: Chronic pancreatitis is a rare cause of portal hypertension. As hepatic pathology mostly contributes to the same. Extrahepatic portal hypertension followed by pancreatitis is a rare condition with most patients being asymptomatic. Objective: This paper aims to present clinical presentation, diagnosis and management of extrahepatic portal hypertension because of chronic pancreatitis. Case Study: A 40-year-old male presented with chief complaints of pain epigastrium and nausea from past 3-4 days which was sudden in onset, progressive in nature, severe in intensity radiating to the back, aggravating on taking food, relieved on leaning forwards and associated with nausea. Results: Clinical features, radiological and other investigations suggested rare diagnosis. Conclusion: Extrahepatic portal hypertension is an important cause of the upper gastrointestinal bleed. Pancreatic aetiology should be considered and most of the times it asymptomatic.