Background: Basidiobolomycosis is a rare fungal infection caused by Basidiobolus ranarum. The Zygomycetes includes two fungal orders: Mucorales and Entomophthorales, with completely different pathogenic potentials. asidiobolusranarum was firs tdescribed in 1886 in frogs. We present a case of bleeding per rectum in a 3-year-old male patient, resident of Southwestern of Saudi Arabia. The diagnosis was confirmed by characteristic histopathlogical findings. The aim of presenting the case is to increase awareness among health care professionals in areas of endemicity, so appropriate specimen processing may lead to enhanced case detection and reporting. Conclusion: Antifungal therapy is adequate to cure Gastrointestinal Basidiobolomycosis infection if the fugal mass is unrespectable.